Keywords
IgG4 related disease; IgG4 tubulointerstitial nephritis; IgG4 biliary sclerosis, IgG4 autoimmune pancreatitis
Abstract
Our case demonstrates the classic imaging features of IgG4-related kidney disease, autoimmune pancreatitis, and sclerosing cholangitis through endoscopic retrograde cholangio-pancreatography (ERCP), ultrasound, CT, and MRI. Immunoglobulin G4 (IgG4) disease is gaining increasing recognition in the medical community as a result of its multi-system involvement. The pancreas remains the most common organ involved in autoimmune pancreatitis (AIP) although, pancreatic involvement is not necessary in order to have extrapancreatic manifestations. Due to its tumefactive nature, accurate diagnosis of IgG4 multi-organ related disease is vital in ensuring appropriate treatment and reduced morbidity associated with unnecessary investigation and intervention.
Citation
Zaleski A, Forbes N, Sawhney S (2019) Igg4 Tubulointerstitial Nephritis and its Role in the Diagnosis of Multi-Organ Igg4 Related Dis ease. SM J Clin Med Imaging 5: 6.