Keywords
Accessory; urethra; phallus; scrotum; Scenarios
Abstract
Introduction: We presented 4 cases managed and operated with varied clinical scenarios; accessory urethra, accessory phallus and accessory scrotum, the study encountered these rare anomalies describing our findings for both anatomical and morphological variations.
Methods: All studied cases were operated in single pediatric surgery unit. All workup was done on basis of clinical presentation accordingly. All patients arranged for chromosomal karyotyping and evaluation of SRY and ATL1 gene loci on X and Y chromosome respectively using polymerase chain reaction amplification PCR. All sites excised sent for histopathology.
Results: Case 1: An 8-months old infant was evaluated for a history of purulent discharge from the opening of the sinus in the midline pre pubic area on the dorsal radix of the penis. Case 2: A 3- days old baby was presented with a mass in the gluteal region with bisexual ambiguity. On evaluation, both vaginal structure and welldeveloped phallus (small penis attached parasitic twin caudally) were present. Case 3: A 4-months old male infant presented with caudal mass (cystic perineal structure) grossly resembling testicle with well prominent phallus covering the anal opening. Case 4: A 2-year old male baby presented with a neighboring ipsilateral bulging peduncular perineal mass resembling phallus measuring 4.7 cm in length and 1.3 cm in width with narrow meatus and a history of drippling urine from this phallus like.
Conclusion: Crucial workup must be submitted including clinical, radiological, chromosomal karyotyping and cytogenic study to asses and resolve such scenarios
Citation
Aboud MJ. Accessory Urethra, Accessory Phallus and Accessory Scrotum; Varied Clinical Scenarios. SM J Pediatr Surg. 2016; 2(6): 1035.