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SM Journal of Pediatric Surgery

Massive Ribs Fractures Due to Artriohepatic Dysplasia (Alagille Syndrome): A Case Report

[ ISSN : 2573-3419 ]

Abstract
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Received: 16-Feb-2018

Accepted: 06-Mar-2018

Published: 08-Mar-2018

Case Report | Volume 4 - Issue 1 | Article DOI :

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Mohammed J Aboud¹, Manal M Kadhim², Shaima Mohammed³, and Noor Abudi⁴

¹Consultant Pediatric Surgery, the Maternity and Child Teaching Hospital, Iraq

²Department of Microbiology, Al Qadisiya University, Iraq

³Pediatrics Specialists, the Maternity and Child Teaching Hospital, Al Diwaniya, Iraq

?Doctor, the Maternity and Child Teaching Hospital, Al Diwaniya, Iraq

Corresponding Author:

Mohammed J Aboud, Consultant pediatric Surgery, The Maternity and Child Teaching Hospital, Iraq, Tel: +964 7801019353; Email: mohammedabud@yahoo.com

Keywords

Ribs Fractures; Artriohepatic Dysplasia; Alagille Syndrome

Abstract

Alagille Syndrome (ALGS) is a rare multisystem congenital disorder, with a minimum incidence of approximately 1:30,000 live births. Several of the characteristics of Alagille syndrome may result in patients having an especially high risk of fracture. Case presentation; a 6-months-old girl admitted to pediatric surgery unit with jaundice since one month of age, progressive abdominal distention. She had been diagnosed with biliary atresia at the age of 1 month on the base of clinical diagnosis; she was malnourished with stunted growth. She had most of the features of Alagille syndrome. Chest radiographs showed generalized decreased in bone density with multiple ribs fractures on the left side, with pulmonary consolidation in the left middle and lower zone. Osteodystrophy (hepatic cause) was enrolled based on the fact that there was no evidence or history of trauma (child abuse by the family was not considered). Our study is one of a few reports to document ribs fracture in children with AGLS.

Citation

Aboud MJ, Kadhim MM, Mohammed S and Abudi N. Massive Ribs Fractures Due to Artriohepatic Dysplasia (Alagille Syndrome): A Case Report. SM J Pediatr Surg. 2018; 4(1): 1060.