Nipple adenoma is a very uncommon, benign proliferative process of lactiferous ducts of the nipple. It commonly presents unilaterally as a palpable nodule in the nipple or an erosive, scaly lesion of the nipple, with or without discharge. Resemblance to other conditions, such as Paget’s disease of the breast, psoriasis, eczema or tumors of the breast can delay diagnosis. The gold standard for treatment is surgical excision; however, newer modalities such as Mohs microsurgery and cryotherapy have been used in limited cases. In this report, we present a case of nipple adenoma and a review of the current literature.