Submit Article
Back to Journal

SM Journal of Pediatrics

Acquired Meningocoele due to Langerhans Cell Histiocytosis

[ ISSN : 3067-9990 ]

Abstract
Details

Received: 20-Mar-2018

Accepted: 21-Mar-2018

Published: 22-Mar-2018

Clinical Image | Volume 3 - Issue 1 | Article DOI :

Download PDF

Shreya Sengupta* and Sayantan Bose

Department of Pediatrics, RG Kar Medical College, India

Corresponding Author:

Shreya Sengupta, Department of Pediatrics, RG Kar Medical College, India, Tel: +917278605066;

Keywords

s Langerhans cells histiocytosis; Acquired meningocoele, Punched out lesions; Unifocal polyostotic LCH

Abstract

Langerhans cells histiocytosis is a relatively common ailment in pediatric age group. Common presentations include bone pain, pathological fractures, skin and scalp eruptions, features of pancytopenia and lymphadenopathy. Sometimes there can be chronic cough and shortness of breath due to lung infiltration. Acquired meningocoele is a rare presenting feature for this disease. Here we present one such case of unifocalpolyostotic Langerhans cells histiocytosis in a 16 year old male patient who had acquired a meningocele. Investigations showed multiple punched out lesions in skull and lytic lesions in several bones but the lung field was cleared. Biopsy and histochemistry confirmed the diagnosis. However the child was found to be HIV positive for which treatment was started but he developed renal failure due to hypercalcemia and died.

Citation

Sengupta S and Bose S. Acquired Meningocoele due to Langerhans Cell Histiocytosis. SM J Pediatr. 2018; 3(1): 1016.